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Anti-ACADM antibody produced in rabbit
半岛bd体育手机客户端 性质
biological source【生物来源】 |
rabbit
|
Quality Level【质量水平】 |
100
|
antibody product type |
primary antibodies
|
clone【克隆】 |
monoclonal
|
form【形式】 |
liquid
|
species reactivity |
human, mouse
|
concentration【浓度】 |
0.6 mg/mL
|
technique(s) |
immunohistochemistry: 1:50-1:200
western blot: 1:500-1:2000 |
UniProt accession no.【UniProt登记号】 |
P11310
|
shipped in【运输】 |
wet ice
|
storage temp.【储存温度】 |
?20℃
|
Gene Information |
human ... ACADM(34)
|
基本信息
General description【一般描述】 |
This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]
|
Immunogen【免疫原】 |
A synthesized peptide derived from human ACADM
|
Physical form【外形】 |
Buffer: PBS with 0.02% sodium azide,0.05% BSA,50% glycerol,pH7.3.
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