2-Hydroxy-2-methylbutanoicacid是一种非正常的代谢物,和羟基戊二酸尿症以及枫糖尿病有关。
Cas No. |
3739-30-8 |
别名 |
2-羟基-2-甲基丁酸 |
Canonical SMILES |
CCC(C)(O)C(O)=O |
分子式 |
C5H10O3 |
分子量 |
118.13 |
溶解度 |
Soluble in DMSO |
储存条件 |
Store at -20°C |
General tips |
For obtaining a higher solubility , please warm the tube at 37 ℃ and shake it in the ultrasonic bath for a while. |
Shipping Condition |
Evaluation sample solution : ship with blue ice All other available size: ship with RT , or blue ice upon request |
半岛bd体育手机客户端 描述 |
2-Hydroxy-2-methylbutanoic acid, an unusual metabolite, is associated with 2-hydroxyglutaric aciduria and maple syrup urine disease. [1]. Dekant W, et al. Biotransformation of MTBE, ETBE, and TAME after inhalation or ingestion in rats and humans. Res Rep Health Eff Inst. 2001 May;(102):29-71; discussion 95-109. |